Kaushal Ashutosh, Haldar Rudrashish, Ambesh Paurush
Department of Anaesthesiology, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Lucknow, Uttar Pradesh, India.
Department of Internal Medicine, Moti Lal Nehru Medical College, Allahabad, Uttar Pradesh, India.
Anesth Essays Res. 2015 Sep-Dec;9(3):443-6. doi: 10.4103/0259-1162.158514.
Achondroplasia is a congenital, disfiguring condition which is the most common form of short-limbed dwarfism. Defective cartilage formation is the hallmark of this condition, which results in a wide spectrum of skeletal abnormalities including spinal defects. Various other systems such as cardiac, pulmonary, and neurological can be simultaneously affected adversely including airway defects. Anesthetic management of such individuals is complicated because of their multisystem affliction. Concomitant atlantoaxial dislocation can further amplify the difficulty during the administration of anesthesia in such patients. We report the successful anesthetic conduct of such a patient with the positive outcome.
软骨发育不全是一种先天性致残疾病,是短肢侏儒症最常见的形式。软骨形成缺陷是这种疾病的标志,会导致一系列骨骼异常,包括脊柱缺陷。心脏、肺部和神经系统等其他各种系统也可能同时受到不利影响,包括气道缺陷。由于这些患者存在多系统疾病,其麻醉管理很复杂。同时存在的寰枢椎脱位会进一步增加此类患者麻醉时的难度。我们报告了对一名此类患者成功实施麻醉并取得良好结果的情况。