Sugrue Jeremy J, Cohen Stephanie B, Marshall Roland M, Riker Adam I
Department of Surgery, University of Illinois at Chicago, Chicago, IL.
Department of Surgery, Advocate Cancer Institute, Advocate Christ Medical Center, Oak Lawn, IL.
Ochsner J. 2015 Winter;15(4):468-72.
Desmoid tumors are relatively uncommon tumors, and those occurring sporadically and in an intraabdominal location are especially rare. Although desmoid tumors have a benign histologic appearance and lack the ability to metastasize, they can invade locally, often aggressively, grow to large sizes, and recur repeatedly.
We present the case of a symptomatic, giant mesenteric desmoid tumor discovered incidentally during workup for the patient's previous history of lung cancer. The patient elected to undergo palliative resection of the tumor because of persistent and unrelenting abdominal pain.
Because of the rarity of the disease, no clear evidence-based guidelines exist for the treatment of sporadic mesenteric desmoid tumors. Review of the available literature suggests that surgical resection with negative margins is a reasonable approach for patients with symptomatic tumors.
韧带样瘤是相对罕见的肿瘤，散发性且发生于腹腔内的韧带样瘤尤为罕见。尽管韧带样瘤具有良性的组织学表现且无转移能力，但它们可局部侵袭，常呈侵袭性生长，体积增大，并反复复发。
我们报告一例有症状的巨大肠系膜韧带样瘤病例，该病例是在对患者既往肺癌病史进行检查时偶然发现的。由于持续性腹痛且疼痛不断加剧，患者选择接受肿瘤姑息性切除术。
由于该疾病罕见，对于散发性肠系膜韧带样瘤的治疗尚无明确的循证指南。对现有文献的回顾表明，切缘阴性的手术切除是有症状肿瘤患者的一种合理治疗方法。
