Dhull V S, Passah A, Rana N, Arora S, Mallick S, Kumar R
Department of Nuclear Medicine, All India Institute of Medical Sciences, New Delhi, India.
Department of Radiodiagnosis, M S Ramaiah Medical College, Bengaluru, India.
Rev Esp Med Nucl Imagen Mol. 2016 Jul-Aug;35(4):260-2. doi: 10.1016/j.remn.2015.09.005. Epub 2015 Dec 28.
A 30-year-old female presented with a 3-month history of erosive stomatitis and bullous lesions, along with recurrent episodes of abdominal pain. She was found to have a retroperitoneal lump in left lumbar region. Skin biopsy revealed bullous disorder. CT guided biopsy of the retroperitoneal mass was suggestive of inflammatory myofibroblastic tumor (IMT). She was started on oral steroids and supportive care, and surgery was being planned when she developed respiratory failure. CT chest revealed vertebral metastases. PET/CT for whole body work up revealed a left para-aortic mass along with multiple skeletal metastases. The patient was kept on conservative management. After 3 months, the patient has shown clinical improvement, and an exploratory laparotomy is now being planned for the excision of the tumor, followed by chemotherapy. This case of retroperitoneal IMT is rare in terms of skeletal metastases with paraneoplastic pemphigus.
一名30岁女性，有3个月的糜烂性口腔炎和大疱性病变病史，伴有反复发作的腹痛。她被发现左腰区有一个腹膜后肿块。皮肤活检显示为大疱性疾病。CT引导下的腹膜后肿块活检提示为炎性肌纤维母细胞瘤（IMT）。她开始接受口服类固醇和支持治疗，在计划手术时出现了呼吸衰竭。胸部CT显示椎体转移。全身PET/CT检查显示左主动脉旁肿块以及多处骨骼转移。患者接受了保守治疗。3个月后，患者临床症状有所改善，现计划进行剖腹探查术切除肿瘤，随后进行化疗。就伴有副肿瘤性天疱疮的骨骼转移而言，这种腹膜后IMT病例很罕见。
