右心室多发性平滑肌瘤：平滑肌瘤的一种罕见形式。

Multiple Primary Leiomyomas in the Right Ventricle: A Rare Form of Leiomyoma.

机构信息

Department of Cardiac Surgery, Zhongshan Hospital, Fudan University, Shanghai, China.

Department of Pathology, Zhongshan Hospital, Fudan University, Shanghai, China.

出版信息

Ann Thorac Surg. 2016 Feb;101(2):e33-5. doi: 10.1016/j.athoracsur.2015.06.114.

DOI:10.1016/j.athoracsur.2015.06.114

PMID:26777967

Abstract

A case of multiple benign leiomyomas in the right ventricle of a 47-year-old woman is presented. Multiple lesions were revealed at different locations in the right ventricle; 1 lesion extended into the right pulmonary artery. Histologic examination showed benign leiomyomas arising from the tunica media of the intramyocardial vessels. Also, the primary origin of the cardiac tumors is demonstrated by the evidence that no leiomyoma was found in the genital system 30 months after the cardiac operation. To our knowledge, this is the first case report of multiple primary cardiac leiomyomas in a premenopausal woman. The midterm prognosis after complete resection is good.

摘要

现报告 1 例 47 岁女性右心室多发良性平滑肌瘤。右心室不同部位发现多个病灶；1 个病灶延伸至右肺动脉。组织学检查显示良性平滑肌瘤起源于心肌内血管的中膜。此外，心脏肿瘤的原发部位也得到了证实，即心脏手术后 30 个月，生殖系统未发现平滑肌瘤。据我们所知，这是首例绝经前女性多发原发性心脏平滑肌瘤的病例报告。完全切除后的中期预后良好。