Ugan Y, Sahin M, Dogru A, Bayram D, Ceyhan A M, Tunc S E
Departments of Internal Medicine, Division of Rheumatology. Suleyman Demirel University Faculty of Medicine, Isparta, Turkey.
Departments of Dermatology. Suleyman Demirel University Faculty of Medicine, Isparta, Turkey.
Clin Ter. 2015 Nov-Dec;166(6):253-5. doi: 10.7417/CT.2015.1897.
Inflammatory myopathies are a heterogeneous group of diseases with unknown etiology characterized by inflammation of the skeletal muscles and proximal muscle weakness. Dermatomyositis (DM) is an idiopathic inflammatory myopathy with characteristic cutaneous findings such as heliotrope rash, Gottron's sign, Gottron's papules, shawl sign and machinist hand. Amyopathic dermatomyositis (ADM) is a rare but well-recognized clinical subtype of DM, constituting aproximately 10-20% of patients with this disease. It generally manifests only pathognomonic skin findings without clinical and laboratory evidence of muscle involvement. In this report, we present a rare case of ADM associated with interstitial pulmonary disease.
炎性肌病是一组病因不明的异质性疾病，其特征为骨骼肌炎症和近端肌无力。皮肌炎（DM）是一种特发性炎性肌病，具有特征性的皮肤表现，如向阳疹、Gottron征、Gottron丘疹、披肩征和技工手。无肌病性皮肌炎（ADM）是DM一种罕见但已得到充分认识的临床亚型，约占该病患者的10%-20%。它通常仅表现出特征性的皮肤表现，而无肌肉受累的临床和实验室证据。在本报告中，我们呈现了1例与间质性肺疾病相关的罕见ADM病例。
