Paluzzi Daniel, Peters Tess, Haber Richard M
School of Medicine, Queen's University, Kingston, ON, Canada.
Division of Dermatology, University of Calgary, Calgary, AB, Canada.
J Cutan Med Surg. 2016 Jul;20(4):349-51. doi: 10.1177/1203475416629406. Epub 2016 Jan 25.
Lipodystrophia centrifugalis abdominalis infantilis (LCAI) is an uncommon dermatological condition characterized by a centrifugally expanding area of lipoatrophy involving the lower abdominal area and is frequently associated with inguinal lymphadenopathy. The average age of onset is 4 years and female individuals from Japan, China, and Korea are affected more often.
To report the first case of LCAI in a Vietnamese patient.
A complete clinical assessment was done and a biopsy from the affected area was performed.
There was an atrophic, slightly hyperpigmented patch at the lower abdomen with prominent underlying vasculature. Inguinal lymphadenopathy was noted on the ipsilateral side. A biopsy showed a lobular panniculitis with fat necrosis and lymphohistiocytic infiltrate with scattered plasma cells and multinucleated giant cells.
To our knowledge, this is the first reported case of LCAI in a Vietnamese patient.
婴儿离心性腹部脂肪营养不良（LCAI）是一种罕见的皮肤病，其特征是下腹部出现离心性扩大的脂肪萎缩区域，且常伴有腹股沟淋巴结病。平均发病年龄为4岁，来自日本、中国和韩国的女性患者更常受累。
报告越南首例LCAI病例。
进行了全面的临床评估，并对受累区域进行了活检。
下腹部有一个萎缩、轻度色素沉着的斑块，其下可见明显的血管。同侧可见腹股沟淋巴结病。活检显示为小叶性脂膜炎，伴有脂肪坏死以及淋巴细胞、组织细胞浸润，并散在有浆细胞和多核巨细胞。
据我们所知，这是越南首例报告的LCAI病例。
