Lee S, Houh W, Kim Y K, Chun S I, Cho B K
Dermatologica. 1982 Feb;164(2):95-100. doi: 10.1159/000250072.
8 Korean children exhibited well-defined depressed lesions of the skin accompanied by slight redness of the surrounding area. First these lesions appeared in the inguinal area and then spread peripherally to the navel region and the ipsilateral vulval area. In these 8 cases, 7 occurred in girls and 1 in a boy. The age of onset ranged from 2 to 9 years. Biopsy specimens taken from the well-depressed area showed a decrease in or absence of, subcutaneous fat and a mild inflammatory infiltrate of lymphocytes and histiocytes in the lower dermis and subcutis. These 8 cases are the first, to our knowledge, to be reported outside Japan and considering the age of onset of the dermatosis it is not confined to infants. Therefore, we would like to describe this entity under the title of lipodystrophia centrifugalis abdominalis juvenilis instead of lipodystrophia centrifugalis abdominalis infantilis.
8名韩国儿童出现了边界清晰的皮肤凹陷性病变,周围区域伴有轻微发红。这些病变首先出现在腹股沟区,然后向周围扩散至肚脐区域和同侧外阴区。在这8例病例中,7例为女孩,1例为男孩。发病年龄在2至9岁之间。从凹陷明显区域获取的活检标本显示皮下脂肪减少或缺失,真皮下部和皮下有轻度淋巴细胞和组织细胞炎性浸润。据我们所知,这8例是日本以外首次报道的病例,考虑到这种皮肤病的发病年龄,它并不局限于婴儿。因此,我们想将这种病症称为青少年离心性腹部脂肪营养不良,而不是婴儿离心性腹部脂肪营养不良。