儿童肠道淋巴管扩张症。对饮食调整的良好反应。

Isa Hasan M, Al-Arayedh Ghadeer G, Mohamed Afaf M

Department of Pediatrics, Salmaniya Medical Complex, Manama, Bahrain. E-mail.

Saudi Med J. 2016 Feb;37(2):199-204. doi: 10.15537/smj.2016.2.13232.

Intestinal lymphangiectasia (IL) is a rare disease characterized by dilatation of intestinal lymphatics. It can be classified as primary or secondary according to the underlying etiology. The clinical presentations of IL are pitting edema, chylous ascites, pleural effusion, acute appendicitis, diarrhea, lymphocytopenia, malabsorption, and intestinal obstruction. The diagnosis is made by intestinal endoscopy and biopsies. Dietary modification is the mainstay in the management of IL with a variable response. Here we report 2 patients with IL in Bahrain who showed positive response to dietary modification.

肠淋巴管扩张症（IL）是一种罕见疾病，其特征为肠淋巴管扩张。根据潜在病因，它可分为原发性或继发性。IL的临床表现有凹陷性水肿、乳糜性腹水、胸腔积液、急性阑尾炎、腹泻、淋巴细胞减少、吸收不良和肠梗阻。诊断通过肠道内镜检查和活检进行。饮食调整是IL治疗的主要方法，但其效果因人而异。在此，我们报告巴林的2例IL患者，他们对饮食调整表现出阳性反应。