Thapaliya Ishwor, Yadav Jeshika
Tribhuvan University, Institute of Medicine, Maharajgunj, Nepal.
Ann Med Surg (Lond). 2024 Feb 28;86(4):2049-2057. doi: 10.1097/MS9.0000000000001850. eCollection 2024 Apr.
Primary intestinal lymphangiectasia (PIL) is a rare disorder in children causing protein-losing enteropathy. Vitamin D deficiency and hypomagnesemia contributed to the tetany. The literature review reflects the importance of screening for these deficiencies and regular serum magnesium monitoring in PIL cases with neuromuscular or ionic abnormalities.
原发性肠淋巴管扩张症(PIL)是一种在儿童中引发蛋白丢失性肠病的罕见病症。维生素D缺乏和低镁血症导致了手足搐搦。文献综述反映了在患有神经肌肉或离子异常的PIL病例中筛查这些缺乏症以及定期监测血清镁的重要性。