Gyedu A
East Afr Med J. 2012 Jan;89(1):34-6.
Neurofibromas are benign tumours arising from neurons andperineural cells. Although they are common inneurofibromatosis, occasionally solitary neurofibromas may occur. A rare case of solitary neurofibroma presenting as a giant gluteal mass in a male patient without a personal or family history of neurofibromatosis is presented. Pre-operative imaging gave useful information about the extent of the mass which was then totally excised with histology revealing a non-plexiform neurofibroma. Distinguishing between isolated neurofibromas and those associated with neurofibromatosis is important because the treatment and prognosis differ greatly with the former having a good prognosis after total excision.
神经纤维瘤是起源于神经元和神经周细胞的良性肿瘤。虽然它们在神经纤维瘤病中很常见，但偶尔也会出现孤立性神经纤维瘤。本文报告了一例罕见的孤立性神经纤维瘤病例，该病例表现为一名男性患者的巨大臀肌肿块，该患者无神经纤维瘤病的个人或家族史。术前影像学检查提供了有关肿块范围的有用信息，随后对肿块进行了完整切除，组织学检查显示为非丛状神经纤维瘤。区分孤立性神经纤维瘤和与神经纤维瘤病相关的神经纤维瘤很重要，因为治疗方法和预后差异很大，前者在完整切除后预后良好。
