Rupprecht V E, Kabus M, Schwarze R
Kinderarztl Prax. 1989 Nov;57(11):545-51.
Within a period of 3 years 4 mature male neonates were observed with an unusual complex of symptoms: subvesical obstruction (valve) with spontaneous pneumothorax/pneumomediastinum. All infants showed immediately postnatal respiratory insufficiency. There are pathogenetical relations between renal and urinary tract malformations and pulmonary changes, which are recognized in Potter's sequence with pulmonary hypoplasia. The authors postulate a deranged dynamic of pulmonary fluid by oligohydramnios, causing increased vulnerable lungs also in such cases without typical x-ray signs of pulmonary hypoplasia. A spontaneous pneumothorax/pneumomediastinum in newborn infants should be the sign to perform nephro-urologic (sonographic) examination.
在3年的时间里,观察到4例成熟男性新生儿出现了一组不寻常的复杂症状:膀胱下梗阻(瓣膜)伴自发性气胸/纵隔气肿。所有婴儿出生后立即出现呼吸功能不全。肾和尿路畸形与肺部变化之间存在病因学关系,这在伴有肺发育不全的波特序列中得到认可。作者推测羊水过少导致肺液动力学紊乱,即使在没有典型肺发育不全X线征象的情况下,也会使肺部变得更加脆弱。新生儿自发性气胸/纵隔气肿应作为进行肾-泌尿外科(超声)检查的指征。