Liu Peng, Xu Ya, Lv Xianli, Ge Huijian, Lv Ming, Li Youxiang
Department of Interventional Neuroradiology, Beijing Neurosurgical Institute and Beijing Tiantan Hospital, Capital Medical University, China.
Department of Neurosurgery, The Third People Hospital in Yancheng City, China.
Interv Neuroradiol. 2016 Jun;22(3):362-4. doi: 10.1177/1591019916632371. Epub 2016 Feb 24.
The pathogenic association between cavernous dural arteriovenous fistula (CDAVF) and moyamoya disease remains unclear. This unusual case is the first report of a progression of unilateral moyamoya disease resulting in the spontaneous occlusion of ipsilateral CDAVF. A 52-year-old woman presented with two-week spontaneous exophthalmos, chemosis and tinnitus, and cerebral angiography showed a right CDAVF coexisting with ipsilateral moyamoya disease. Transvenous approaches through the inferior petrosal sinus and facial vein were attempted but failed. However, a progression of the moyamoya disease and disappearance of the CDAVF were observed on one month follow-up angiogram in accordance with the resolution of clinical symptoms. This extremely rare coincidental presentation may have deeper pathogenic implications. This case report may give a clue to the underlying mechanism of the progression of moyamoya disease and occlusion of the CDAVF.
海绵窦硬脑膜动静脉瘘（CDAVF）与烟雾病之间的致病关联仍不明确。这一罕见病例是关于单侧烟雾病进展导致同侧CDAVF自发闭塞的首例报告。一名52岁女性出现了为期两周的自发性眼球突出、结膜水肿和耳鸣，脑血管造影显示右侧CDAVF与同侧烟雾病并存。尝试通过岩下窦和面部静脉的经静脉入路，但未成功。然而，在一个月的随访血管造影中，随着临床症状的缓解，观察到烟雾病进展且CDAVF消失。这种极其罕见的巧合表现可能具有更深层次的致病意义。本病例报告可能为烟雾病进展和CDAVF闭塞的潜在机制提供线索。
