Coupris L, Germouty I, Granry J C, Varlet F, Desnos J
Service de Chirurgie Pédiatrique, CHRU Angers.
Chir Pediatr. 1989;30(5):181-6.
Congenital tracheoesophageal fistulas (CTOF) without esophageal atresia are uncommon and exceptional when multiple. Authors report a new personal case treated in two times. Others eight cases in literature are studied. Only one pre-operative diagnosis was made. Two old no-operated cases were discovered at autopsy. For five, no clinical modification was noted after the first CTOF surgical care. In them two no-reoperated died and the second fistula was seen after. For the others, the same radiological or endoscopic exams that have not marked the second fistula were positive after surgery. No explanation was done. For a better result, systematic complete investigation of trachea and esophagus are necessary even if first fistula is diagnosed. Luckily per-operative discovery of second fistula (one case) do not allowed initial extensive surgery. To support a second congenital tracheoesophageal fistula after a surgical time, many criterias are necessary: 1. a undoubted fistula recognised during the first intervention; 2. recurrent symptoms after surgery with no free interval; 3. identification by radiology or endoscopy of a new tracheoesophageal shunt in other place that the first; 4. its surgical discovery in no previous dissected area. In all cases where fistulas are described, the aspect is not the same: the upper fistula is a "H" type and the lower is shorter and larger ("X" type). To note a case of three simultaneaous fistulas in the same patient.
先天性食管气管瘘(CTOF)且无食管闭锁的情况较为罕见,若为多发则更为特殊。作者报告了一例分两次治疗的新病例,并对文献中的其他八例病例进行了研究。仅做出了一例术前诊断。两例未手术的旧病例在尸检时被发现。其中五例在首次CTOF手术治疗后未观察到临床变化。其中两例未再次手术的患者死亡,第二处瘘管在之后被发现。对于其他病例,术前未显示第二处瘘管的相同影像学或内镜检查在术后呈阳性,但未作解释。为获得更好的结果,即使已诊断出第一处瘘管,也有必要对气管和食管进行系统全面的检查。幸运的是,术中发现第二处瘘管(一例)避免了最初的广泛手术。为支持术后出现第二处先天性食管气管瘘,需要多个标准:1. 在首次干预期间识别出明确的瘘管;2. 术后出现反复症状且无间歇期;3. 通过影像学或内镜检查在不同于第一处的其他部位识别出新的气管食管分流;4. 在之前未解剖的区域通过手术发现。在所有描述有瘘管的病例中,其形态各不相同:上部瘘管为“H”型,下部瘘管较短且较大(“X”型)。值得注意的是,同一患者出现三处同时存在的瘘管的病例。