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干燥综合征患者出现多种类型环形红斑的抗信号识别颗粒抗体阳性多发性肌炎:环形红斑与肌炎活动之间的正相关。

Anti-signal recognition particle antibody-positive polymyositis in a patient with Sjögren's syndrome showing various types of annular erythema: Positive correlation between the activities of annular erythema and myositis.

作者信息

Kabuto Miho, Fujimoto Noriki, Hamaguchi Yasuhito, Tanaka Toshihiro

机构信息

Department of Dermatology, Shiga University of Medical Science, Otsu, Japan.

Department of Dermatology, Graduate School of Medical Science, Kanazawa University, Kanazawa, Japan.

出版信息

J Dermatol. 2016 Aug;43(8):958-61. doi: 10.1111/1346-8138.13344. Epub 2016 Mar 12.

Abstract

Annular erythema with Sjögren's syndrome (AESS) is occasionally found, especially in Asian patients, which is classified into three types. We present a case of Sjögren's syndrome showing various types of AESS with anti-signal recognition particle antibody-positive polymyositis. We successfully treated the eruption and myositis with a low dose of prednisolone. Every onset of annular erythema coincided with elevation of serum creatine kinase levels, which suggests the correlation between the activities of annular erythema and polymyositis.

摘要

伴有干燥综合征的环形红斑(AESS)偶尔会被发现,尤其是在亚洲患者中,它可分为三种类型。我们报告一例干燥综合征患者,其表现为各种类型的AESS并伴有抗信号识别颗粒抗体阳性的多发性肌炎。我们用低剂量泼尼松龙成功治疗了皮疹和肌炎。每次环形红斑发作都与血清肌酸激酶水平升高同时出现,这表明环形红斑和多发性肌炎的活动之间存在相关性。

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