Kumar Santosh, Bishnoi Kshitij, Murugavaithianathan Pragatheeswarane, Panwar Vikas Kumar
Department of Urology, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
J Clin Imaging Sci. 2016 Feb 26;6:6. doi: 10.4103/2156-7514.177552. eCollection 2016.
Castleman's disease is a rare, benign lymphoproliferative disorder of unknown origin. Paraneoplastic pemphigus is a common association which presents as oral mucosal ulcerations. Abdominal and retroperitoneal Castleman's disease present either as a localized disease or as a systemic disease. We hereby present a 15-year-old male patient with oral mucosal lesions with localized vague right lower abdominal mass who was diagnosed to have Castleman's disease with paraneoplastic pemphigus which was surgically excised.
卡斯尔曼病是一种罕见的、病因不明的良性淋巴增生性疾病。副肿瘤性天疱疮是一种常见的伴发疾病,表现为口腔黏膜溃疡。腹部和腹膜后卡斯尔曼病可表现为局限性疾病或全身性疾病。我们在此报告一名15岁男性患者,有口腔黏膜病变,右下腹有局限性模糊肿块,诊断为卡斯尔曼病伴副肿瘤性天疱疮,已通过手术切除。