Hilmani Said, Ngamasata Trezor, Karkouri Mehdi, Elazahri Abdessamad
Department of Neurosurgery, Ibn Rochd UHC, Hassan II University, Casablanca, Morocco.
Department of Anatomic Pathology, Ibn Rochd UHC, Hassan II University, Casablanca, Morocco.
Surg Neurol Int. 2016 Mar 2;7(Suppl 5):S153-5. doi: 10.4103/2152-7806.177892. eCollection 2016.
Paraganglioma of the filum terminale is an uncommon tumor of cauda equina region. Lumbar radiculopathies are revelations that can get complicated from cauda equina syndrome. Magnetic resonance imaging (MRI) allows the diagnosis without distinguishing it from a neurofibroma. Only histopathological study can bring certainty in the diagnosis. The treatment of choice is a complete removal.
We report a case of paraganglioma of the filum terminale in a 74-year-old female patient, admitted for cauda equina syndrome, which has been progressing for 2 years. MRI of medulla objectified an extramedullary lesion at L3-L4, diagnosed as neurinoma. A complete resection of the tumor was performed with a section of the filum terminale, which she was taking since birth. Histology confirmed the diagnosis of paraganglioma. The clinical course was characterized by a complete recovery of the deficit.
Through this case report, the authors discuss clinical and radiological aspects of this tumor, as well as the management in the light of published data.
终丝副神经节瘤是马尾神经区域一种罕见的肿瘤。腰椎神经根病是马尾神经综合征可能出现的并发症。磁共振成像(MRI)虽能做出诊断,但无法将其与神经纤维瘤区分开来。只有组织病理学研究才能明确诊断。首选治疗方法是完整切除。
我们报告一例74岁女性患者的终丝副神经节瘤病例,该患者因马尾神经综合征入院,病情已进展2年。脊髓MRI显示L3 - L4水平有髓外病变,诊断为神经鞘瘤。手术完整切除肿瘤并切断患者自出生就有的终丝。组织学检查确诊为副神经节瘤。临床病程表现为功能缺损完全恢复。
通过本病例报告,作者结合已发表的数据讨论了该肿瘤的临床和放射学特征以及治疗方法。