Tranos P, Dervenis N, Kiouras S
a Ophthalmica Eye Institute , Thessaloniki , Greece.
Semin Ophthalmol. 2017;32(4):501-503. doi: 10.3109/08820538.2015.1123732. Epub 2016 Apr 14.
To describe a case of bilateral cystoid macular edema in a patient with Dandy-Walker syndrome. An 18-year-old male was referred to our tertiary referral center for evaluation of his decreased visual acuity. Detailed ophthalmic examination and imaging revealed the presence of bilateral cystoid macular edema, which was successfully treated with intravitreal triamcinolone injections (2 mg in 0.05 ml). Recurrence of macular edema developed after a period of approximately four months. This is an unusual ophthalmic manifestation of Dandy-Walker syndrome. Cystoid macular edema should be included in the differential diagnosis of subjects with Dandy-Walker syndrome presenting with decreased vision. The pathogenetic mechanism for the development macular edema in this case is not clear. Intravitreal triamcinolone is an effective treatment, but edema was recurrent in our case. Other approaches (such as oral Acetazolamide or intravitreal Anti-VEGF) have to be considered as well.
描述一例患有丹迪-沃克综合征患者的双侧囊样黄斑水肿病例。一名18岁男性因视力下降被转诊至我们的三级转诊中心进行评估。详细的眼科检查和影像学检查发现存在双侧囊样黄斑水肿，通过玻璃体内注射曲安奈德（0.05 ml中含2 mg）成功治疗。大约四个月后黄斑水肿复发。这是丹迪-沃克综合征一种不寻常的眼科表现。囊样黄斑水肿应纳入丹迪-沃克综合征视力下降患者的鉴别诊断中。该病例中黄斑水肿发生的发病机制尚不清楚。玻璃体内注射曲安奈德是一种有效的治疗方法，但在我们的病例中水肿复发了。也必须考虑其他治疗方法（如口服乙酰唑胺或玻璃体内注射抗血管内皮生长因子）。
