Wieliczko Monika, Dylewska Magdalena
Katedra i Klinika Nefrologii, Dializoterapii i Chorób Wewnętrznych, Warszawski Uniwersytet Medyczny, Warszawa.
Wiad Lek. 2015;68(4 Pt 2):626-30.
Pulmonary-renal syndrome is rare disease. The term describes acute syndrome is ANCA associated vasculitis. The patients need aggressive therapy (induction and maintenance phase), in some cases accompanied by plasmapheresis. They often have respiratory failure and require dialysis because of acute kidney injury.
肺肾综合征是一种罕见疾病。该术语描述的是与抗中性粒细胞胞浆抗体(ANCA)相关血管炎的急性综合征。患者需要积极治疗(诱导期和维持期),某些情况下还需进行血浆置换。他们常因急性肾损伤出现呼吸衰竭并需要透析。