Noushad S Navin, Rajaraman R, Shanmugam Subbiah
Surgical Oncology, Govt. Royapettah Hospital, Chennai, India.
Dept. of Surgical Oncology, Govt. Royapettah Hospital, Chennai, India.
Int J Surg Case Rep. 2016;24:10-3. doi: 10.1016/j.ijscr.2016.04.045. Epub 2016 May 4.
Lesser sac pathological entities are uncommon. Most of these are tumors and are generally misdiagnosed as retroperitoneal lesions.
A 62year old male with past history of treated hypopharyngeal cancer presented with progressive abdominal distension. Physical examination revealed a midline intra abdominal mass in the epigastrium and umbilical region. Radiological investigations were suggestive of a retroperitoneal tumor,an image guided biopsy was reported as atypical lipoma. Surgical exploration confirmed a large multi lobulated tumor arising primarily from the lesser sac, post operative histopathological examination confirmed a myxoid liposarcoma.
Primary lesser sac tumors are rare, a literature review of primary lesser sac tumors with particular reference to myxoid liposarcoma is presented.
Primary lesser sac liposarcomas are rare neoplasms. The myxoid variant is unique for its peculiar biological behavior, in its sensitivity to chemotherapy and radiotherapy and for the presence of specific cytogenetic marker.
小网膜囊病理实体并不常见。其中大多数是肿瘤,通常被误诊为腹膜后病变。
一名62岁男性,既往有下咽癌治疗史,出现进行性腹胀。体格检查发现上腹部和脐区中线腹内肿块。影像学检查提示为腹膜后肿瘤,影像引导下活检报告为非典型脂肪瘤。手术探查证实一个主要起源于小网膜囊的大的多叶状肿瘤,术后组织病理学检查证实为黏液样脂肪肉瘤。
原发性小网膜囊肿瘤罕见,本文对原发性小网膜囊肿瘤,特别是黏液样脂肪肉瘤进行了文献综述。
原发性小网膜囊脂肪肉瘤是罕见肿瘤。黏液样变体因其独特的生物学行为、对化疗和放疗的敏感性以及特定细胞遗传学标志物的存在而独具特点。