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一名右位心合并主动脉瓣环扩张成年患者的保留瓣膜手术

Valve sparing surgery in an adult patient with dextrocardia and annuloaortic ectasia.

作者信息

Zeybek Rahmi, Bacaksiz Ahmet, Sharifov Rasul, Sevgili Emrah, Ay Yasin

机构信息

Department of Cardiovascular Surgery, Faculty of Medicine, BezmiÂlem Foundation University, Istanbul, Turkey.

Department of Cardiology, Faculty of Medicine, BezmiÂlem Foundation University, Istanbul, Turkey.

出版信息

Kardiochir Torakochirurgia Pol. 2016 Mar;13(1):42-4. doi: 10.5114/kitp.2016.58964. Epub 2016 Mar 30.

DOI:10.5114/kitp.2016.58964
PMID:27212978
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4860434/
Abstract

We report the case of a patient with situs inversus totalis, annuloaortic ectasia complicated by aortic insufficiency and mitral regurgitation which induced congestive heart failure. Both valvular lesions were repaired physiologically using aortic root sparing Yacoub 'remodeling' technique and mitral ring annuloplasty. Valve sparing techniques can be used effectively even in patients with complicated clinical scenarios (like dextrocardia and annuloaortic ectasia) to avoid the potential risks related to prosthetic valve implantation and lifelong anticoagulation therapy.

摘要

我们报告了一例全内脏转位患者的病例,该患者患有主动脉环扩张并伴有主动脉瓣关闭不全和二尖瓣反流,进而引发了充血性心力衰竭。采用保留主动脉根部的亚库布“重塑”技术和二尖瓣环成形术对两个瓣膜病变进行了生理性修复。即使在临床情况复杂的患者(如右位心和主动脉环扩张)中,保留瓣膜技术也能有效应用,以避免与人工瓣膜植入和终身抗凝治疗相关的潜在风险。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ae/4860434/710ab99e00f0/KITP-13-58964-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ae/4860434/f4bb94e3d84d/KITP-13-58964-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ae/4860434/710ab99e00f0/KITP-13-58964-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ae/4860434/f4bb94e3d84d/KITP-13-58964-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/63ae/4860434/710ab99e00f0/KITP-13-58964-g002.jpg

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本文引用的文献

1
Aortic valve sparing operations in aortic root aneurysms: remodeling or reimplantation?主动脉根部动脉瘤的保留主动脉瓣手术:重塑还是再植入?
Ann Cardiothorac Surg. 2013 Jan;2(1):44-52. doi: 10.3978/j.issn.2225-319X.2013.01.14.
2
Cardiac surgery for annuloaortic ectasia and mitral regurgitation in an adult patient with dextrocardia.一名右位心成年患者因主动脉瓣环扩张和二尖瓣反流接受心脏手术。
Gen Thorac Cardiovasc Surg. 2011 May;59(5):341-3. doi: 10.1007/s11748-010-0682-z. Epub 2011 May 6.
3
A population-based study of cardiac malformations and outcomes associated with dextrocardia.
右旋心及全内脏转位患者主动脉瓣置换术的左侧入路
J Saudi Heart Assoc. 2017 Oct;29(4):297-299. doi: 10.1016/j.jsha.2017.03.007. Epub 2017 Mar 24.
一项基于人群的关于右位心相关心脏畸形及预后的研究。
Am J Cardiol. 2007 Jul 15;100(2):305-9. doi: 10.1016/j.amjcard.2007.02.095. Epub 2007 May 25.
4
Mitral valve repair versus replacement in simultaneous mitral and aortic valve surgery for rheumatic disease.风湿性疾病患者同期二尖瓣和主动脉瓣手术中二尖瓣修复与置换的比较。
Ann Thorac Surg. 2007 Feb;83(2):558-63. doi: 10.1016/j.athoracsur.2006.08.015.
5
Dextrocardia: an analysis of cardiac structures in 125 patients.右位心:125例患者心脏结构分析
Int J Cardiol. 2003 Apr;88(2-3):143-55; discussion 155-6. doi: 10.1016/s0167-5273(02)00539-9.