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Recurrent pneumomediastinum in adult dermatomyositis.

作者信息

Cicuttini F M, Fraser K J

机构信息

Austin Hospital, Rheumatology Unit, Heidelberg, Australia.

出版信息

J Rheumatol. 1989 Mar;16(3):384-6.

PMID:2724255
Abstract

A muscle biopsy established the diagnosis of dermatomyositis in a 22-year-old woman with normal muscle enzyme levels, 18 months after she presented with constitutional symptoms, a rash and polyarthritis. Her subsequent course was complicated by cutaneous ulcers with histological changes suggesting vasculitis, interstitial pulmonary involvement and recurrent pneumomediastinum, the latter being recently reported in 2 other cases of dermatomyositis. Cutaneous vasculitis has been present in all cases and it is suggested that the pneumomediastinum may be due to pulmonary vasculitis.

摘要

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