Sano S, Brawn W J, Mee R B
Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Australia.
J Thorac Cardiovasc Surg. 1989 Jun;97(6):886-92.
Forty-four patients with total anomalous pulmonary venous drainage underwent repair between 1979 and 1987. The anomalous drainage was supracardiac in 16, cardiac in 12, and infracardiac in 16. Median age at repair was 15 days and median weight, 3.3 kg. In 22 patients (50%) the venous drainage was obstructed. Emergency operation was necessary in 12 patients, and the condition of seven additional patients deteriorated while they were awaiting semiurgent operation. There was one hospital death (mortality rate 2.3%), occurring in a 2-week-old premature neonate with infracardiac drainage. In 17 of 44 patients, mean pulmonary artery pressure equaled or exceeded systemic arterial pressure immediately after repair. Four patients have required reoperation and two of these have died as a result of peripheral extension of pulmonary vein sclerosis. In the review period of from 1 month to 7 years, all survivors are well and receiving no medication.
1979年至1987年间，44例完全性肺静脉异位引流患者接受了修复手术。其中，心上型异位引流16例，心内型12例，心下型16例。修复手术时的中位年龄为15天，中位体重为3.3千克。22例患者（50%）存在静脉引流梗阻。12例患者需要急诊手术，另有7例患者在等待半急诊手术期间病情恶化。有1例医院死亡（死亡率2.3%），发生在1名2周大的患有心下型引流的早产新生儿身上。44例患者中有17例在修复手术后即刻平均肺动脉压等于或超过体动脉压。4例患者需要再次手术，其中2例因肺静脉硬化外周扩展而死亡。在1个月至7年的随访期内，所有幸存者情况良好，未服用任何药物。
