Héry E, Jimenez M, Didier D, van Doesburg N H, Guérin R, Fouron J C, Davignon A
Section of Cardiology and Radiology, Sainte-Justine Hospital, University of Montreal, Quebec, Canada.
Am J Cardiol. 1989 Jun 1;63(18):1385-9. doi: 10.1016/0002-9149(89)91053-9.
The anatomy of superior-inferior ventricles was studied in 17 patients, aged 1 day to 22 years, using echocardiography and angiography. In all patients, the right ventricle was located superiorly and the left ventricle inferiorly. The right ventricular sinus was underdeveloped in 14 of the 17 patients. Conversely, the right ventricular outflow tract was normally developed in all 17 patients. The visceroatrial situs was solitus in all patients, and it was associated with a concordant D-loop in 9 patients and with a discordant L-loop in 8. There was a high incidence of associated transposition of the great arteries (9 patients) or double-outlet right ventricle (5). Segmental combination was unpredictable, D-loop being associated with L-position of the great arteries in 4 of 8 patients and L-loop being associated with D-position of the great arteries in 4 of 9. There were only 3 concordant ventriculoarterial connections. Frequently associated anomalies included ventricular septal defect (17 patients), atrioventricular valve malformations (17) subaortic conus (14) and pulmonary outflow tract stenosis or atresia (11). Criss-cross hearts were present in only 7 patients.
对17例年龄从1天至22岁的患者进行了上下心室解剖学研究，采用了超声心动图和血管造影术。在所有患者中，右心室位于上方，左心室位于下方。17例患者中有14例右心室窦发育不全。相反，17例患者的右心室流出道均发育正常。所有患者的内脏心房位置正常，其中9例为一致的D袢，8例为不一致的L袢。合并大动脉转位（9例）或右心室双出口（5例）的发生率较高。节段组合不可预测，8例患者中有4例D袢与大动脉L位相关，9例患者中有4例L袢与大动脉D位相关。仅有3例心室动脉连接一致。常见的合并畸形包括室间隔缺损（17例）、房室瓣畸形（17例）、主动脉下圆锥（14例）和肺流出道狭窄或闭锁（11例）。仅7例患者存在交叉心脏。
