Lee Kimberley, Shah Nishant P, Christenson Eric S, Zakaria Sammy, Okwuosa Ike
Department of Medicine, Johns Hopkins University School of Medicine, 4940 Eastern Avenue, Baltimore, MD 21224, USA.
Future Cardiol. 2016 Jul;12(4):467-70. doi: 10.2217/fca-2016-0005. Epub 2016 Jun 13.
Decompensated heart failure affects 5 million Americans and nearly 15 million individuals worldwide. Heart failure can be attributed to numerous etiologies, with autoimmune conditions representing a rare category of acute decompensations. Here, we report of case of a 66-year-old woman who presented with acute decompensated heart failure as a result of a rare vasculitis known as idiopathic aortitis. In addition to describing the case, we highlight the importance of proper ascending aorta evaluation in patients presenting with new onset heart failure, especially in the setting of aortic regurgitation. We use this case to discuss the entity of idiopathic aortitis, and review the literature on its clinical manifestations and long-term management.
失代偿性心力衰竭影响着500万美国人以及全球近1500万人。心力衰竭可归因于多种病因,自身免疫性疾病是急性失代偿的罕见类型。在此,我们报告一例66岁女性病例,该患者因一种罕见的血管炎——特发性主动脉炎而出现急性失代偿性心力衰竭。除了描述该病例外,我们强调了对新发心力衰竭患者,尤其是伴有主动脉反流的患者进行升主动脉正确评估的重要性。我们利用该病例讨论特发性主动脉炎的实体,并回顾其临床表现和长期管理的相关文献。