Joyce Kenneth M, O'hEireamhoin Sven, Sheng Michael Tan Chien, Devitt Aiden
Department of Trauma & Orthopaedic Surgery, Galway University Hospital, Galway, Ireland.
Division of Anatomic Pathology, Department of Histopathology, Galway University Hospital, Galway, Ireland.
J Orthop Case Rep. 2014 Apr-Jun;4(2):73-7. doi: 10.13107/jocr.2250-0685.173.
Involvement of the spinal column in either monostotic or polyostotic form is rare, with fewer than thirty-five cases discussed in the literature. Most of the cases of polyostotic fibrous dysplasia of spine have involvement of the appendicular skeleton.
We report a case of a 74-year-old Irish man with a two month history of back pain. Investigations revealed a diagnosis of fibrous dysplasia involving three levels of the thoracic spine in isolation. The patient underwent T2-T9 stabilization and bone grafting.
A case of fibrous dysplasia involving three levels of the thoracic spine in isolation has never previously been reported. The extreme rarity of this type of presentation can pose a diagnostic dilemma, and in cases with spinal involvement, a consensus of management has not yet been achieved.
脊柱以单发性或多发性形式受累较为罕见,文献中讨论的病例少于35例。大多数脊柱多发性骨纤维发育不良病例累及附属骨骼。
我们报告一例74岁爱尔兰男性,有两个月背痛病史。检查发现诊断为孤立性累及胸椎三个节段的骨纤维发育不良。患者接受了T2-T9节段的固定和植骨手术。
此前从未有过孤立性累及胸椎三个节段的骨纤维发育不良病例的报告。这种表现形式极为罕见,可能会造成诊断难题,对于脊柱受累的病例,尚未达成管理共识。