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脊髓内神经结节病

Intramedullary spinal neurosarcoidosis.

作者信息

Saadi Altaf, Rajashekara Shruthi

出版信息

Radiol Case Rep. 2015 Dec 7;7(4):739. doi: 10.2484/rcr.v7i4.739. eCollection 2012.

DOI:10.2484/rcr.v7i4.739
PMID:27330596
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4899563/
Abstract

Neurosarcoidosis is a rare diagnosis, and it is also unusual for a patient with sarcoidosis to present solely with neurologic disease. However, CNS involvement can be the first manifestation of disease in 50% of patients. Thus, it is an important diagnostic consideration in patients presenting with ambiguous nervous-system lesions, particularly in the population most often affected by sarcoidosis: young African-Americans. We report a case of a 32-year-old African-American male with spinal sarcoidosis presenting as bilateral upper-extremity and upper-trunk parasthesias secondary to an intramedullary spinal lesion.

摘要

神经结节病是一种罕见的诊断,结节病患者仅表现为神经系统疾病也不常见。然而,中枢神经系统受累可能是50%患者疾病的首发表现。因此,对于出现不明原因神经系统病变的患者,尤其是在结节病最常累及的人群——年轻非裔美国人中,这是一个重要的诊断考虑因素。我们报告一例32岁非裔美国男性脊髓结节病病例,表现为双侧上肢和上躯干感觉异常,继发于脊髓髓内病变。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/c18692bf444a/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/120804c6abed/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/82f298ce9a88/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/6e97796ea906/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/c18692bf444a/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/120804c6abed/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/82f298ce9a88/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/6e97796ea906/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/eaa0/4899563/c18692bf444a/gr4.jpg

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本文引用的文献

1
Magnetic resonance imaging of neurosarcoidosis.神经结节病的磁共振成像
J Clin Imaging Sci. 2011;1:15. doi: 10.4103/2156-7514.76693. Epub 2011 Feb 11.
2
Spinal neurosarcoidosis.脊髓结节病
Acta Neurol Taiwan. 2011 Jun;20(2):142-8.
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Clinical features of spinal cord sarcoidosis: analysis of 17 neurosarcoidosis patients.脊髓结节病的临床特征:17 例神经结节病患者分析。
J Neurol. 2011 Dec;258(12):2163-7. doi: 10.1007/s00415-011-6080-3. Epub 2011 May 7.
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Correlation of MR imaging findings and clinical manifestations in neurosarcoidosis.神经结节病的磁共振成像表现与临床表现的相关性
AJNR Am J Neuroradiol. 2009 May;30(5):953-61. doi: 10.3174/ajnr.A1470. Epub 2009 Feb 4.
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Extramedullary spinal neurosarcoidosis: report of two cases.髓外脊髓神经结节病:两例报告
Eur Neurol. 2005;54(4):220-4. doi: 10.1159/000090714. Epub 2006 Jan 6.
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Spinal neurosarcoidosis mimicking an idiopathic inflammatory demyelinating syndrome.酷似特发性炎性脱髓鞘综合征的脊髓结节病
Arch Neurol. 2004 Apr;61(4):586-9. doi: 10.1001/archneur.61.4.586.
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Imaging manifestations of neurosarcoidosis.神经结节病的影像学表现。
AJR Am J Roentgenol. 2004 Feb;182(2):289-95. doi: 10.2214/ajr.182.2.1820289.
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Clinical characteristics of patients in a case control study of sarcoidosis.结节病病例对照研究中患者的临床特征
Am J Respir Crit Care Med. 2001 Nov 15;164(10 Pt 1):1885-9. doi: 10.1164/ajrccm.164.10.2104046.