Megachoroid as a cause of isolated ventricle syndrome.

Recent sonographic studies have demonstrated enlarged choroid plexuses to be an abnormality associated with myelomeningocele. We report a patient with hydrocephalus and myelomeningocele who had huge bilateral enlargement of the choroid plexuses which were large enough to occlude the foramen of Monro of the shunted and collapsed ventricle. It produced an isolated ventricle syndrome leading to the need for bilateral ventriculoperitoneal shunts.