Maruyama K, Tanaka M, Ikeda S, Tada T, Yanagisawa N
Rinsho Shinkeigaku. 1989 Jan;29(1):108-11.
A patient, 30-year-old man, was admitted to Shinshu University Hospital with gait disturbance and numbness of both arms and legs in June 1985. General physical findings were normal except for facial asymmetry, i.e. mild right facial hemiatrophy. Blood pressure was normal and there were no signs of arteriosclerosis. Neurological examination revealed marked bilateral pyramidal tract signs, muscular weakness of all extremities predominant of the right side, spastic gait and sensory disturbance with impairment of pin prick and light touch sensation in the second and third trigeminal nerve regions and extremities of the left side, and mild loss of vibratory sense and numbness in all extremities. X-ray examination of the cervical spine and the myelogram of the spinal canal were normal. CT scan of the brain performed 3 hours after the myelography showed that the left vertebral artery extended from the left side of the medulla oblongata to the midline and distorted it by compression. MRI confirmed the findings of the CT scan. Vertebral angiography disclosed that the elongated left vertebral artery crossed the ventral aspect of the medulla oblongata. Compression of the medulla oblongata by the vertebral artery was diagnosed and neurovascular decompression was performed. About one month after the operation his spastic gait and muscular weakness were slightly improved, but these symptoms progressed thereafter. One year after operation his spastic gait was more marked than preoperatively. In many cases with dolichoectatic intracranial arteries, hypertension and arteriosclerosis have been reported to be usually associated with this condition. In other opinions dolichoectasia has been suggested to be a congenital disease, because such vessels are occasionally present in children.(ABSTRACT TRUNCATED AT 250 WORDS)
一名30岁男性患者于1985年6月因步态障碍及双上肢和双下肢麻木入住信州大学医院。除面部不对称,即轻度右侧面部萎缩外,全身体格检查结果正常。血压正常,无动脉硬化迹象。神经学检查发现明显的双侧锥体束征、四肢肌肉无力(右侧为主)、痉挛性步态以及感觉障碍,左侧三叉神经第二和第三区域及四肢针刺觉和轻触觉减退,四肢轻度振动觉丧失和麻木。颈椎X线检查及椎管造影正常。脊髓造影后3小时进行的脑部CT扫描显示,左侧椎动脉从延髓左侧延伸至中线并压迫使其变形。MRI证实了CT扫描结果。椎动脉造影显示延长的左侧椎动脉越过延髓腹侧。诊断为椎动脉对延髓的压迫,并进行了神经血管减压术。术后约1个月,他的痉挛性步态和肌肉无力稍有改善,但此后这些症状仍有进展。术后1年,他的痉挛性步态比术前更明显。在许多颅内动脉冗长扩张的病例中,据报道高血压和动脉硬化通常与此病症相关。另一些观点认为,冗长扩张可能是一种先天性疾病,因为这种血管偶尔在儿童中也会出现。(摘要截取自250字)