Suzuki Hiroyuki, Kakurai Keigo, Morishita Seita, Kimura Daisaku, Fukumoto Masanori, Sato Takaki, Kida Teruyo, Ueki Mari, Sugasawa Jun, Ikeda Tsunehiko
Department of Ophthalmology, Osaka Medical College, Takatsuki City, Japan.
Department of Ophthalmology, Osaka Medical College, Takatsuki City, Japan; Department of Ophthalmology, Yao Tokushukai Hospital, Yao City, Japan.
Case Rep Ophthalmol. 2016 Jun 13;7(2):333-40. doi: 10.1159/000446638. eCollection 2016 May-Aug.
The purpose of this study was to report a case of Von Hippel-Lindau disease (VHL) with twin retinal capillary hemangiomas that was successfully treated by vitreous surgery for tractional retinal detachment following laser photocoagulation.
A 44-year-old male presented at our university hospital after noticing decreased visual acuity in his right eye. The patient had previously undergone multiple operations for cerebellar, thoracic, and lumbar spine hemangioblastomas when he was approximately 19 years old. Upon initial examination, ocular findings revealed twin connected retinal capillary hemangiomas around the temporal upper area of the patient's right eye. The patient was subsequently diagnosed with VHL based on his medical history and current observations of the ocular fundus. Tractional retinal detachment had occurred as the result of the formation of proliferative membranes following laser photocoagulation. The patient underwent vitreous surgery to treat the tractional retinal detachment, resulting in a successful postoperative outcome.
The findings of this study show the possibility that proliferative changes and tractional retinal detachment can arise following photocoagulation for retinal capillary hemangiomas in patients with VHL.
本研究旨在报告一例患有双眼视网膜毛细血管瘤的冯·希佩尔-林道病（VHL）患者，该患者在激光光凝术后因牵引性视网膜脱离接受玻璃体手术并获得成功治疗。
一名44岁男性因右眼视力下降就诊于我院。该患者在约19岁时曾因小脑、胸椎和腰椎的血管母细胞瘤接受过多次手术。初次检查时，眼部检查发现患者右眼颞上区域周围有相连的双眼视网膜毛细血管瘤。根据患者的病史和目前眼底检查结果，随后诊断为VHL。激光光凝后增殖膜形成导致牵引性视网膜脱离。患者接受玻璃体手术治疗牵引性视网膜脱离，术后效果良好。
本研究结果表明，VHL患者视网膜毛细血管瘤光凝后可能出现增殖性改变和牵引性视网膜脱离。
