Thawani Jayesh P, Randazzo Michael J, Singh Nickpreet, Pisapia Jared M, Abdullah Kalil G, Storm Phillip B
Department of Neurosurgery, Hospital of the University of Pennsylvania, Philadelphia, Pennsylvania, United States.
Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States.
J Neurol Surg Rep. 2016 Jul;77(3):e118-20. doi: 10.1055/s-0036-1586211.
Cervical teratomas are rare germ cell tumors affecting the fetus that are associated with significant morbidity and mortality due to an increased risk of airway obstruction at delivery. These tumors can commonly produce polyhydramnios that results from the fetus' impaired ability to swallow amniotic fluid. Improved rates of prenatal diagnosis through comprehensive evaluations and imaging have dramatically impacted the perinatal management of infants with this condition. Here, we report a patient diagnosed with polyhydramnios whose fetus was discovered to have a giant cervical teratoma on imaging studies. The child underwent surgical resection after having the airway secured under the uteroplacental support as part of an ex utero intrapartum treatment procedure performed at 37 weeks. The following gross pathological and magnetic resonance images demonstrate this condition and its currently accepted treatment.
颈部畸胎瘤是一种罕见的影响胎儿的生殖细胞肿瘤,由于分娩时气道阻塞风险增加,与显著的发病率和死亡率相关。这些肿瘤通常会导致羊水过多,这是由于胎儿吞咽羊水的能力受损所致。通过全面评估和成像提高产前诊断率,对患有这种疾病的婴儿的围产期管理产生了巨大影响。在此,我们报告一例诊断为羊水过多的患者,其胎儿在影像学检查中被发现患有巨大颈部畸胎瘤。该患儿在37周时作为子宫外产时治疗程序的一部分,在子宫胎盘支持下确保气道安全后接受了手术切除。以下大体病理和磁共振图像展示了这种疾病及其目前公认的治疗方法。