Shiner Elizabeth A, Zagami Alessandro S
Institute of Neurological Sciences, Prince of Wales Hospital, Randwick, NSW, Australia.
Institute of Neurological Sciences, Prince of Wales Hospital, Randwick, NSW, Australia; Prince of Wales Clinical School, UNSW, Kensington, NSW, Australia.
SAGE Open Med Case Rep. 2014 Nov 14;2:2050313X14559638. doi: 10.1177/2050313X14559638. eCollection 2014.
Primary angiitis of the central nervous system is a rare idiopathic vasculitis affecting small- and medium-sized vessels, isolated to the brain, leptomeninges and spinal cord. We report a case of biopsy-proven primary angiitis of the central nervous system, displaying some atypical features. This case highlights several key diagnostic and management issues of the disorder as well as its potential heterogeneity.
中枢神经系统原发性血管炎是一种罕见的特发性血管炎,累及中小血管,仅发生于脑、软脑膜和脊髓。我们报告一例经活检证实的中枢神经系统原发性血管炎病例,该病例具有一些非典型特征。该病例突出了该疾病的几个关键诊断和管理问题及其潜在的异质性。