Ravishankar Chitra
Division of Cardiology, The Perelman School of Medicine at the University of Pennsylvania, The Children's Hospital of Philadelphia, Philadelphia, PA.
Pediatr Crit Care Med. 2016 Aug;17(8 Suppl 1):S344-6. doi: 10.1097/PCC.0000000000000825.
To describe the various surgical options, perioperative management strategies, and outcomes for this complex lesion.
MEDLINE and PubMed.
L-transposition of the great arteries is a relatively rare defect, comprising less than 1% of all congenital heart defects. There is considerable heterogeneity in clinical presentation depending on the presence of associated defects. Surgery for this rare and complex defect has evolved from "physiologic" repair in which the right ventricle remains in the systemic position to the "anatomic" repair, which restores the left ventricle as the systemic ventricle. There has been a great interest in performing the anatomic repair or "double switch" operation, a rather complex operation that presents unique challenges in the postoperative period.
描述针对这种复杂病变的各种手术选择、围手术期管理策略及结果。
MEDLINE和PubMed。
大动脉L型转位是一种相对罕见的缺陷，占所有先天性心脏缺陷的比例不到1%。根据是否存在相关缺陷，临床表现存在很大异质性。针对这种罕见且复杂的缺陷的手术已从“生理性”修复（右心室仍处于体循环位置）发展到“解剖性”修复，即将左心室恢复为体循环心室。人们对进行解剖性修复或“双调转”手术（一种相当复杂的手术，在术后阶段带来独特挑战）有着浓厚兴趣。
