Da Silva Jose Pedro, Da Silva Luciana Fonseca, Baumgratz Jose Francisco, Castro Rodrigo Moreira, Bezerra Rodrigo Freire, Guilhen Jose Cicero
Department of Cardiovascular Surgery, Hospital Beneficencia Portuguesa of São Paulo, Brazil; Paulista School of Medicine, Federal University of Sao Paulo, Brazil.
Department of Cardiovascular Surgery, Hospital Beneficencia Portuguesa of São Paulo, Brazil; Paulista School of Medicine, Federal University of Sao Paulo, Brazil.
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2015;18(1):34-9. doi: 10.1053/j.pcsu.2015.01.005.
The pulmonary root translocation (PRT) procedure has been used to correct ventriculoarterial discordance or malposition of great arteries since 1994. It was part of the surgical repair of 62 consecutive patients presenting with congenitally corrected transposition of the great arteries (CCTGA) with ventricular septal defect (VSD) and pulmonary stenosis (PS), or other complex congenital heart disease with malposition of the great arteries, VSD, and PS. PRT was performed as follows: removal of the pulmonary artery (PA) with the pulmonary valve from its abnormal position, closure of the consequent hole with an autologous pericardial patch, resection of some conal septum, creation of an intraventricular tunnel connecting the left ventricle to the aorta, and construction of a new right ventricular outflow tract using the translocated PA. In patients presenting with important pulmonary valve stenosis, the pulmonary artery was enlarged with a monocusp valve pericardial patch. The Senning procedure was used with some modification to complete the anatomical repair in CCTGA patients. Overall in-hospital and long-term mortality were 4.8% and 3.4%, respectively. PRT appears to be a good surgical alternative for patients presenting with CCTGA with VSD and PS, and other lesions involving malposition of the great arteries, VSD, and PS.
自1994年以来,肺动脉根部移位术(PRT)一直用于纠正心室动脉不一致或大动脉错位。它是62例连续患者手术修复的一部分,这些患者患有先天性矫正型大动脉转位(CCTGA)并伴有室间隔缺损(VSD)和肺动脉狭窄(PS),或患有其他伴有大动脉错位、VSD和PS的复杂先天性心脏病。PRT的操作如下:将肺动脉(PA)及其肺动脉瓣从异常位置移除,用自体心包补片封闭随之产生的孔洞,切除部分圆锥隔,建立连接左心室与主动脉的室内隧道,并使用移位的PA构建新的右心室流出道。对于存在严重肺动脉瓣狭窄的患者,用单瓣心包补片扩大肺动脉。对Senning手术进行了一些改良,用于完成CCTGA患者的解剖修复。总体住院死亡率和长期死亡率分别为4.8%和3.4%。对于患有CCTGA并伴有VSD和PS以及其他涉及大动脉错位、VSD和PS的病变的患者,PRT似乎是一种很好的手术选择。