García Cecilia, Álvarez Teresa, Bravo Coral, Pérez-Caballero Ramón, Viadero María Teresa, Gámez Francisco, Pérez Ricardo, De León-Luis Juan
Department of Obstetrics and Gynecology, Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain.
Department of Pediatric Cardiology, Hospital General Gregorio Marañón, Universidad Complutense de Madrid, Madrid, Spain.
J Ultrasound Med. 2016 Oct;35(10):2087-93. doi: 10.7863/ultra.15.11021. Epub 2016 Aug 8.
A prenatal aortopulmonary window with an interrupted aortic arch was detected in a 22-week-old fetus. The 3-vessel and trachea view showed a communication between the ascending aorta and the pulmonary artery. Early postnatal surgery was successful. A PubMed-based search identified all cases of prenatal aortopulmonary windows between 2002 and 2015. Nine articles were identified. The average gestational age at diagnosis was 28 weeks (range, 22-33 weeks). The most frequent aortopulmonary window was type I (40%). All cases were associated with congenital heart defects, mainly an interrupted aortic arch (50%). No chromosomal or extracardiac abnormalities were seen. Prenatal echocardiography is useful for early diagnosis of an aortopulmonary window. The prognosis depends on the time of surgery and the nature of the associated anomalies.
在一名22周大的胎儿中检测到产前主肺动脉窗合并主动脉弓中断。三血管和气管视图显示升主动脉与肺动脉之间存在交通。出生后早期手术成功。基于PubMed的检索确定了2002年至2015年间所有产前主肺动脉窗病例。共识别出9篇文章。诊断时的平均孕周为28周(范围22 - 33周)。最常见的主肺动脉窗类型为I型(40%)。所有病例均伴有先天性心脏缺陷,主要是主动脉弓中断(50%)。未发现染色体或心外异常。产前超声心动图有助于早期诊断主肺动脉窗。预后取决于手术时间及相关异常的性质。