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以红白血病告终的特发性骨髓纤维化

Idiopathic myelofibrosis terminating in erythroleukemia.

作者信息

Garcia S, Miguel A, Miguel A, Linares M, Navarro M, Colomina P

机构信息

Hematology Service, Hospital General, Valencia, Spain.

出版信息

Am J Hematol. 1989 Sep;32(1):70-1. doi: 10.1002/ajh.2830320114.

DOI:10.1002/ajh.2830320114
PMID:2757005
Abstract

A 55-year-old woman with a one-year history of idiopathic myelofibrosis progressed to erythroleukemia. This is the first reported occurrence of erythroleukemia progression from idiopathic myelofibrosis. Certain patterns of leukemia transformation from myeloproliferative disorders are favored: Myeloblastic or myelomonocytic. The rare incidence of erythroblastic transformation is discussed.

摘要

一名患有特发性骨髓纤维化一年的55岁女性进展为红白血病。这是首次报道特发性骨髓纤维化进展为红白血病的病例。骨髓增殖性疾病向白血病转化存在某些特定模式:髓母细胞性或粒单核细胞性。文中讨论了红系母细胞转化的罕见发生率。

相似文献

1
Idiopathic myelofibrosis terminating in erythroleukemia.以红白血病告终的特发性骨髓纤维化
Am J Hematol. 1989 Sep;32(1):70-1. doi: 10.1002/ajh.2830320114.
2
Acute myelofibrosis terminating in erythroleukemic state.以红白血病状态告终的急性骨髓纤维化。
Am J Clin Pathol. 1982 Jul;78(1):102-4. doi: 10.1093/ajcp/78.1.102.
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Erythroleukemia with myelofibrosis--pediatric case report and discussion of possible stem cell origin of the disorder.伴有骨髓纤维化的红白血病——儿科病例报告及该疾病可能的干细胞起源探讨
Nihon Ketsueki Gakkai Zasshi. 1985 Sep;48(6):1414-22.
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Wild-type JAK2 secondary acute erythroleukemia developing after JAK2-V617F-mutated primary myelofibrosis.JAK2-V617F突变的原发性骨髓纤维化后发生的野生型JAK2继发性急性红白血病。
Acta Haematol. 2009;122(1):36-8. doi: 10.1159/000235773. Epub 2009 Aug 28.
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The relationship of erythromonocytic leukemia to other myeloproliferative disorders.
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Idiopathic acquired sideroblastic anemia terminating in acute myelofibrosis: case report and review of leterature.特发性获得性铁粒幼细胞贫血终末期并发急性骨髓纤维化:病例报告及文献复习
Cancer. 1977 Jan;39(1):359-65. doi: 10.1002/1097-0142(197701)39:1<359::aid-cncr2820390155>3.0.co;2-c.
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Primary myelofibrosis terminating in myeloblastic transformation within a short time.
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Acute myelofibrosis terminating as acute myeloblastic leukemia.以急性髓系白血病告终的急性骨髓纤维化
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[An autopsy case of primary myelofibrosis terminated in erythroleukemia after splenectomy].[一例原发性骨髓纤维化尸检病例,脾切除术后发展为红白血病]
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Extensive myelofibrosis responsive to treatment for acute erythroblastic leukaemia.对急性红白血病治疗有反应的广泛性骨髓纤维化。
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引用本文的文献

1
Development of acute leukaemia after idiopathic myelofibrosis.特发性骨髓纤维化后急性白血病的发生
J Clin Pathol. 1992 May;45(5):427-30. doi: 10.1136/jcp.45.5.427.