Abou-Al-Shaar Hussam, Bahatheq Ayman, Takroni Radwan, Al-Thubaiti Ibrahim
Department of Neurosciences, Division of Neurological Surgery, King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia; College of Medicine, Alfaisal University, Riyadh, Saudi Arabia.
Department of Neurosciences, Division of Neurological Surgery, King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia.
Surg Neurol Int. 2016 Aug 1;7(Suppl 18):S523-6. doi: 10.4103/2152-7806.187495. eCollection 2016.
Suprasellar cavernous malformation in the optic pathway is not commonly encountered. To date, there are only few reports present in the literature.
The authors report a rare case of suprasellar optic pathway cavernous malformation in a 33-year-old female who presented with progressive visual loss. Her imaging revealed a large heterogeneous, hyperintense, hemorrhagic right suprasellar extra-axial complex cystic structure, causing mass effect on the adjacent hypothalamus and third ventricle displacing these structures. Gross total resection of the lesion was achieved utilizing a right frontal craniotomy approach. Histopathological examination confirmed the diagnosis of suprasellar chiasmal cavernous malformation.
Although visual pathway cavernous malformation is a rare event, it should be included in the differential diagnosis of lesions occurring suprasellarly in the visual pathway and hypothalamus.
视路中上丘脑海绵状畸形并不常见。迄今为止，文献中仅有少数报道。
作者报告了一例罕见的33岁女性视路中上丘脑海绵状畸形病例，该患者出现进行性视力丧失。其影像学检查显示右侧鞍上轴外有一个大的异质性、高信号、出血性复杂囊性结构，对相邻的下丘脑产生占位效应，使第三脑室移位。通过右额开颅手术入路实现了病变的全切除。组织病理学检查证实为鞍上视交叉海绵状畸形。
尽管视路海绵状畸形是一种罕见情况，但在视路和下丘脑鞍上区病变的鉴别诊断中应考虑到。
