口腔组织的乳腺外佩吉特病——文献综述及1例罕见病例报告

Extramammary Paget's disease of the oral tissues-literature review and a rare case report.

作者信息

Kennedy Hana, Kunjur Jayanth, Amarasinghe Kavita, Smith Graham

机构信息

St. George's Hospital, Tooting, SW170QT London, UK

St. George's Hospital, Tooting, SW170QT London, UK.

出版信息

J Surg Case Rep. 2016 Sep 1;2016(9):rjw152. doi: 10.1093/jscr/rjw152.

DOI:10.1093/jscr/rjw152

PMID:27587306

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5007617/

Abstract

Extramammary Paget's disease (EMPD) is a rare, cutaneous adenocarcinoma in situ characterized by a chronic eczema-like rash of the anogenital regions. It is usually slow growing, locally invasive and presents mainly with pruritis. Extremely rare in the oral tissues, here we present a case of EMPD of the hard palate and a review of the existing literature base.

摘要

乳房外佩吉特病（EMPD）是一种罕见的皮肤原位腺癌，其特征为肛门生殖器区域出现慢性湿疹样皮疹。它通常生长缓慢，具有局部侵袭性，主要表现为瘙痒。在口腔组织中极为罕见，在此我们报告一例硬腭EMPD病例并对现有文献进行综述。