切除术后的长期随访强调了手术在原发性肝上皮样血管内皮瘤中的作用。
Long term follow up after resection emphasizes the role of surgery in Primary Hepatic Epithelioid Hemangioendothelioma.
作者信息
Mehrabi Arianeb, Hoffmann Katrin, Weiss Karl Heinz, Mogler Carolin, Schemmer Peter, Büchler Markus W, Alldinger Ingo
机构信息
Department of General, Visceral and Transplantation Surgery, University Hospital Heidelberg, Germany.
Department of Gastroenterology, University Hospital Heidelberg, Germany.
出版信息
Ann Med Surg (Lond). 2016 Mar 10;11:1-4. doi: 10.1016/j.amsu.2016.03.002. eCollection 2016 Nov.
Abstract
BACKGROUND
Primary Hepatic Epithelioid Hemangioendothelioma is an extremely rare tumor of vascular origin.
PATIENTS
In this work we present clinical data and long term results of eight patients who were surgically treated in our institution. Liver transplantation was performed in five patients (four cadaveric and one living related) and major liver resection in three patients. Three patients are alive with recurrent tumor. After a median follow-up of 100 months (48-266) all patients are alive.
CONCLUSIONS
Only surgery can provide cure in HEH. If the extent of the disease prohibits primary resection liver transplantation might offer the most valuable option.
摘要
背景
原发性肝上皮样血管内皮瘤是一种极其罕见的血管源性肿瘤。
患者
在本研究中，我们展示了在我院接受手术治疗的8例患者的临床资料和长期结果。5例患者接受了肝移植（4例尸体供肝和1例活体亲属供肝），3例患者接受了肝大部切除术。3例患者带复发性肿瘤存活。经过中位100个月（48 - 266个月）的随访，所有患者均存活。
结论
只有手术能治愈肝上皮样血管内皮瘤。如果疾病范围不允许一期切除，肝移植可能是最有价值的选择。
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