From the Department of Radiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA.
Clin Nucl Med. 2016 Nov;41(11):899-901. doi: 10.1097/RLU.0000000000001366.
Klippel Trenaunay syndrome commonly manifests as lower limb hypertrophy where vascular malformation occurs. However, up to 20% of patients with Klippel Trenaunay syndrome can have gastrointestinal involvement. An 18-year-old man with known Klippel Trenaunay syndrome in the left lower extremity underwent Tc-labeled red blood cell imaging to determine the site of gastrointestinal bleeding. The images did not reveal the site of active bleeding. However, diffuse non-moving activity in the left abdomen and pelvis was noted, which corresponded to hypertrophied colon and related blood vessels, consistent with intestinal involvement of Klippel Trenaunay syndrome.
克莱佩特伦纳伊综合征通常表现为下肢肥大，伴有血管畸形。然而，高达 20%的克莱佩特伦纳伊综合征患者可能存在胃肠道受累。一名 18 岁男性，左下肢患有已知的克莱佩特伦纳伊综合征，接受 Tc 标记的红细胞成像以确定胃肠道出血部位。图像未显示活动出血部位。然而，左腹部和骨盆弥漫性非移动性活动被注意到，与肥大的结肠和相关血管相对应，符合克莱佩特伦纳伊综合征的肠道受累。
