Serebrakian Arman T, Golinko Michael S, Alperovich Michael, Runyan Christopher M, Staffenberg David A
*Division of Plastic Surgery, Temple University School of Medicine, Philadelphia, PA †Division of Plastic Surgery, Arkansas Children's Hospital, Little Rock, AR ‡Department of Plastic Surgery, New York University Langone Medical Center, New York, NY.
J Craniofac Surg. 2016 Oct;27(7):e673-e676. doi: 10.1097/SCS.0000000000003075.
Craniofacial microsomia remains the second most common craniofacial deformity after cleft lip and palate. Mandibular pathology has been classically scored from type I to type III by the modified Pruzansky-Kaban classification. The authors report a case of a 5-year-old patient with Goldenhar syndrome and bilateral type III craniofacial macrosomia. The patient had absence of bilateral glenoid fossas, condyles, coronoids, and rami as well as hypoplasia of the symphysis, parasymphysis, and mandibular body. Reconstruction was performed using 2 costochondral rib autografts to reconstruct a ramus and assist in the development of a neo-glenoid fossa at the cranial base. An additional portion of costal rib graft was used to augment the deficient symphysis. The patient was placed in class III occlusion postoperatively using maxillo-mandibular fixation screws and heavy elastics. The bone grafts healed without complications with no evidence of ankylosis, nonunion, or resorption to date. For the most severe forms of craniofacial microsomia, costochondral grafting remains an effective initial technique for lengthening the hypoplastic mandible and providing a foundation for future distraction.
颅面短小畸形仍然是继唇腭裂之后第二常见的颅面畸形。下颌骨病变传统上根据改良的普鲁赞斯基-卡班分类法分为I型至III型。作者报告了一例5岁患有戈尔登哈综合征和双侧III型颅面巨大畸形的患者。该患者双侧关节盂窝、髁突、冠突和下颌支缺如,以及联合部、联合旁和下颌体发育不全。使用2块肋软骨自体移植物进行重建,以重建下颌支并协助在颅底形成一个新的关节盂窝。另外一部分肋软骨移植物用于增大发育不全的联合部。术后使用上颌-下颌固定螺钉和粗弹力线将患者置于III类咬合关系。骨移植物愈合良好,无并发症,迄今为止没有强直、骨不连或吸收的迹象。对于最严重形式的颅面短小畸形,肋软骨移植仍然是延长发育不全下颌骨并为未来牵张提供基础的有效初始技术。