Lee Chi-Kyou, Lee Hyun Ju
Department of Otorhinolarygology-Head and Neck Surgery, Soonchunhyang University School of Medicine, Cheonan, Korea.
Department of Pathology, Soonchunhyang University School of Medicine, Cheonan, Korea.
J Audiol Otol. 2016 Sep;20(2):120-2. doi: 10.7874/jao.2016.20.2.120. Epub 2016 Sep 1.
A solitary fibrous tumor (SFT) is an extremely rare, distinct otological soft-tissue tumor. Only two such tumors in the external auditory canal have been reported. A SFT related to hemangiopericytomas (HPC), which commonly arise in the central nervous system. HPCs act malignant in many cases, while SFTs at other sites are mainly benign. A 25-year-old female presented with highly vascular tumor at the right external auditory meatus and bleeding from the mass when a crust was removed from its surface. After excisional biopsy followed by pre-operative embolization, this tumor confirmed with SFT. The recurrence rate of SFT is very low after complete resection, with a slightly increased risk of recurrence with extrathoracic tumors. We describe the third case of SFT in the external auditory canal and review the literature.
孤立性纤维瘤(SFT)是一种极其罕见的独特耳科软组织肿瘤。外耳道仅报道过两例此类肿瘤。SFT与血管外皮细胞瘤(HPC)相关,后者常见于中枢神经系统。HPC在许多情况下表现为恶性,而其他部位的SFT主要为良性。一名25岁女性,右侧外耳道出现高血管性肿瘤,去除表面结痂时肿物出血。经切除活检及术前栓塞后,该肿瘤确诊为SFT。SFT完整切除后的复发率非常低,胸外肿瘤的复发风险略有增加。我们报道外耳道SFT的第三例病例并复习文献。