Brewer Katherine, Attalla Kyrollis, Husain Fatima, Tsao Che-Kai, Badani Ketan K, Sfakianos John P
Icahn School of Medicine at Mount Sinai, Department of Urology, 1 Gustave L. Levy Pl, New York, NY 10029, USA.
Icahn School of Medicine at Mount Sinai, Department of Medical Oncology, 1 Gustave L. Levy Pl, New York, NY 10029, USA.
Urol Case Rep. 2016 Sep 23;9:33-6. doi: 10.1016/j.eucr.2016.08.011. eCollection 2016 Nov.
Primary leiomyosarcomas of the inferior vena cava (IVC) are rare tumors associated with poor prognosis, and surgical resection with the goal of obtaining negative margins is the gold standard for initial treatment. Tumor characteristics of both extraluminal extension into renal parenchyma and intraluminal extension of the subdiaphragmatic IVC are even less common. The prognosis of vascular leiomyosarcomas is determined by the location and the size of the tumor, as these factors determine the risk of local recurrence and metastasis. We present a case of a 30-year old female incidentally found to have a 14 cm right renal mass and IVC thrombus.
原发性下腔静脉平滑肌肉瘤是一种罕见肿瘤,预后较差,以获得切缘阴性为目标的手术切除是初始治疗的金标准。肿瘤向肾实质腔外扩展以及膈下下腔静脉腔内扩展的特征更为少见。血管平滑肌肉瘤的预后取决于肿瘤的位置和大小,因为这些因素决定了局部复发和转移的风险。我们报告一例30岁女性,偶然发现有一个14厘米的右肾肿块和下腔静脉血栓形成。