Milovanovic Vladimir, Stefanovic Igor, Ilic Slobodan
1Department of Pediatric Cardiac Surgery,University Children's Hospital,Belgrade,Serbia.
2Department of Pediatric Cardiology,University Children's Hospital,Belgrade,Serbia.
Cardiol Young. 2017 Apr;27(3):580-583. doi: 10.1017/S1047951116001499. Epub 2016 Sep 29.
The association of tricuspid atresia with aortopulmonary window is exceptionally rare. We report a patient with tricuspid atresia, normally related great arteries, non-restrictive ventricular septal defect, and no pulmonary stenosis (type IC) with an aortopulmonary window who underwent successful initial surgical palliation. The unique anatomical feature of this case, other than the presence of the aortopulmonary window, was the absence of pulmonary stenosis at the level of either the ventricular septal defect or the pulmonary valve. All other reported cases have described some degree of restriction of anterograde pulmonary flow due to pulmonary stenosis or atresia.
三尖瓣闭锁合并主肺动脉窗极为罕见。我们报告一例三尖瓣闭锁患者，其大动脉关系正常，室间隔缺损无限制，无肺动脉狭窄（IC型），合并主肺动脉窗，成功接受了首次手术姑息治疗。除存在主肺动脉窗外，该病例的独特解剖特征是在室间隔缺损或肺动脉瓣水平均无肺动脉狭窄。所有其他已报道的病例均描述了由于肺动脉狭窄或闭锁导致的顺行性肺血流存在一定程度的受限。
