噬血细胞性淋巴组织细胞增生症：一种难以捉摸的综合征。
Haemophagocytic lymphohistiocytosis: an elusive syndrome.
作者信息
Thomas William, Veer Mars Van't, Besser Martin
机构信息
Addenbrooke's Hospital, Cambridge, UK
Addenbrooke's Hospital, Cambridge, UK.
出版信息
Clin Med (Lond). 2016 Oct;16(5):432-436. doi: 10.7861/clinmedicine.16-5-432.
Abstract
Haemophagocytic lymphohistiocytosis is a rare inflammatory condition. It can present in adult general medical patients and is a challenging diagnostic conundrum. This article provides an overview of the pathophysiology and clinical presentation of the syndrome for the general physician who will be rarely confronted with this problem but will have to act promptly when the situation arises. Treatment is also briefly discussed, although this usually occurs in a specialist setting after the diagnosis has been established.
摘要
噬血细胞性淋巴组织细胞增生症是一种罕见的炎症性疾病。它可出现在成年普通内科患者中，是一个具有挑战性的诊断难题。本文为普通内科医生概述了该综合征的病理生理学和临床表现，这类医生很少会遇到这个问题，但一旦出现这种情况必须迅速采取行动。文中也简要讨论了治疗方法，不过这通常是在确诊后在专科环境中进行。
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