Garba Moumouni, Atmani Samir, Sani Rabiou, Nouhou Kaled Adamou
Tunis Med. 2016 Apr;94(4):284-289.
Background From the first description in 1886, significant progress was made on the treatment of Ebstein disease by mono and bi-ventricular surgery. Aim To highlight the prognosis of Ebstein's anomaly in the pediatric department of Hassan II hospital in Fez. Methods This is a descriptive and retrospective study of 4 years. Results We collected nine patients (seven boys and two girls) with a mean age of 5.3 years. Cyanosis was the main mode of revelation of the disease. In three patients Ebstein's anomaly was part of a malformative syndrome. All patients had only symptomatic medical treatment. Five patients are still alive at a follow up of one to six years. Conclusion Symptomatic medical treatment of Ebstein malformation may improve the prognosis of the disease.
背景 自1886年首次描述以来，单心室和双心室手术在埃布斯坦病的治疗方面取得了重大进展。目的 强调非斯哈桑二世医院儿科埃布斯坦畸形的预后。方法 这是一项为期4年的描述性回顾性研究。结果 我们收集了9例患者（7名男孩和2名女孩），平均年龄5.3岁。发绀是该疾病的主要表现形式。3例患者的埃布斯坦畸形是畸形综合征的一部分。所有患者仅接受了对症药物治疗。在1至6年的随访中，5例患者仍然存活。结论 埃布斯坦畸形的对症药物治疗可能改善该疾病的预后。
