左心发育不全综合征：当前观点
Hypoplastic left heart syndrome: current perspectives.
作者信息
Greenleaf Christopher E, Urencio J Miguel, Salazar Jorge D, Dodge-Khatami Ali
机构信息
University of Mississippi Medical Center, 2500 North State Street, Jackson MS 39216, USA.
出版信息
Transl Pediatr. 2016 Jul;5(3):142-147. doi: 10.21037/tp.2016.05.04.
Abstract
Since the first successful intervention for hypoplastic left heart syndrome (HLHS) was undertaken by Norwood in 1983, there have been many advancements in the pre-, intra-, and postoperative care of these children for a diagnosis that just 25 years ago was almost certainly a fatal one. This paper aims to describe the most recent trends and perspectives on the treatment of HLHS. In particular, we will discuss the five current options for HLHS, including Norwood stage I as the beginning to 3-stage palliation, transplant, true hybrid, hybrid-bridge-to-Norwood, and compassionate care.
摘要
自1983年诺伍德首次成功干预治疗左心发育不全综合征（HLHS）以来，对于这些患儿在术前、术中和术后护理方面取得了许多进展，而就在25年前，这种疾病几乎肯定是致命的。本文旨在描述HLHS治疗的最新趋势和观点。特别是，我们将讨论目前治疗HLHS的五种选择，包括作为三阶段姑息治疗开端的诺伍德I期手术、移植、真正的杂交手术、杂交手术过渡到诺伍德手术以及姑息治疗。
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