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Dermatomyositis--Part 1: Definition, Epidemiology, Etiology and Pathogenesis, and Clinics.

作者信息

Ramos-E-Silva Marcia, Pinto Ana Paula Frade Lima, Pirmez Rodrigo, Cuzzi Tullia, Carneiro Sueli Coelho da Silva

机构信息

Sector of Dermatology and Post-Graduation Course in Dermatology;

Sector of Dermatology and Post-Graduation Course in Dermatology.

出版信息

Skinmed. 2016 Aug 1;14(4):273-279. eCollection 2016.

PMID:27784516
Abstract

Dermatomyositis is an inflammatory autoimmune disorder that affects the skin, muscles, and blood vessels. The prevailing clinical manifestations are intense erythema, typically around the eyes and dorsum of the hands, accompanied by proximal muscle weakness. There is one clinical form, called amyopathic dermatomyositis, which lacks muscular symptoms and laboratory evidence of muscle damage.

摘要

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