Urbańska Ewa K, Pawlak Szymon, Grzybowski Adam, Śliwka Joanna, Rycaj Jarosław, Obersztyn-Zawiślan Anna, Wierzyk Arkadiusz, Przybylski Roman
Clinical Department of Cardiac Anesthesia and Intensive Care, School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Silesian Center for Heart Diseases, Zabrze, Poland.
Department of Cardiac Surgery and Transplantation, School of Medicine with the Division of Dentistry in Zabrze, Medical University of Silesia in Katowice, Silesian Center for Heart Diseases, Zabrze, Poland.
Kardiochir Torakochirurgia Pol. 2016 Sep;13(3):269-272. doi: 10.5114/kitp.2016.62622. Epub 2016 Sep 30.
Anomalous origin of the left coronary artery from the pulmonary artery (Bland-White-Garland syndrome - BWG) is a serious congenital cardiac anomaly leading to myocardial ischemia with severe heart failure. Immediate surgical correction is the treatment of choice, and the risk of postoperative complications depends on the degree of myocardial injury. The authors present two cases of infants with BWG, in whom long-term (175 and 26 days) left ventricular assistance with a Berlin Heart device was used, resulting in successful weaning from the support and subsequent hospital discharge. Because of serious hemorrhagic complications and their neurological consequences observed in the first patient, the anticoagulation protocol was modified in the second patient, providing more stable support and allowing the device to be removed after a shorter period of time. The Berlin Heart left ventricular assist device may be treated not only as a bridge for transplantation but also, considering the shortage of donors in this age group, as a bridge to recovery.
左冠状动脉起源于肺动脉（布兰德-怀特-加兰综合征 - BWG）是一种严重的先天性心脏异常，可导致心肌缺血并伴有严重心力衰竭。立即进行手术矫正为首选治疗方法，术后并发症的风险取决于心肌损伤程度。作者介绍了两例BWG婴儿病例，其中使用柏林心脏装置进行了长期（175天和26天）的左心室辅助，最终成功脱离支持并随后出院。由于在首例患者中观察到严重出血并发症及其神经系统后果，因此在第二例患者中修改了抗凝方案，从而提供了更稳定的支持，并允许在更短时间后移除装置。柏林心脏左心室辅助装置不仅可作为移植的桥梁，而且考虑到该年龄组供体短缺的情况，还可作为恢复的桥梁。
