Sharma Girish, Augustyn Cyprian, Nawrocki Paweł, Cichoń Romuald
Lower Silesian Center for Heart Diseases, Wroclaw, Poland.
Student Research Association operating at the Lower Silesian Center for Heart Diseases, Wroclaw, Poland.
Kardiochir Torakochirurgia Pol. 2015 Mar;12(1):77-9. doi: 10.5114/kitp.2015.50576. Epub 2015 Mar 31.
The anomalous origin of the left coronary artery arising from the pulmonary artery (ALCAPA), also known as Bland-White-Garland (BWG) syndrome, is a rare congenital heart disease. We present cases of three children in whom BWG syndrome was repaired surgically. In two of them, the left coronary artery was transplanted from the pulmonary trunk to the aorta, and in one, the Takeuchi procedure was performed. In both cases in which the left coronary artery was transplanted to the aorta, mechanical circulatory support was used after the surgery. This was due to a low ejection fraction (10%) while weaning from cardiopulmonary bypass. Although associated with numerous complications, mechanical circulatory support can be a lifesaving therapy in patients with a poor left ventricular function after the correction of BWG syndrome.
左冠状动脉起源于肺动脉（ALCAPA）异常，也称为布兰德 - 怀特 - 加兰（BWG）综合征，是一种罕见的先天性心脏病。我们报告了三例接受BWG综合征手术修复的儿童病例。其中两例将左冠状动脉从肺动脉干移植到主动脉，一例进行了竹内手术。在将左冠状动脉移植到主动脉的两例病例中，术后均使用了机械循环支持。这是因为在脱离体外循环时射血分数较低（10%）。尽管机械循环支持会引发多种并发症，但对于BWG综合征矫正后左心室功能不佳的患者而言，它可能是一种挽救生命的治疗方法。
