McCreedy C A, Zimmerman T J, Webster S F
Department of Surgery, Kaiser Permanente Medical Center, Oakland, Calif.
Surgery. 1989 Feb;105(2 Pt 1):170-4.
Pseudoxanthoma elasticum is a rare inherited connective tissue disorder, which exhibits genetic heterogeneity. It is characterized by elastic tissue degeneration involving many organ systems, with typical cutaneous, ocular, arterial, and gastrointestinal manifestations. Upper gastrointestinal tract hemorrhage occurs in 13% of patients with pseudoxanthoma elasticum and is often resistant to conventional methods of treatment. A case report involving gastric hemorrhage in a patient with pseudoxanthoma elasticum is presented. The characteristics of pseudoxanthoma elasticum are reviewed, and the management of upper gastrointestinal tract hemorrhage in these patients is discussed.
弹性假黄瘤是一种罕见的遗传性结缔组织疾病，具有遗传异质性。其特征为弹性组织退变，累及多个器官系统，有典型的皮肤、眼部、动脉和胃肠道表现。13%的弹性假黄瘤患者会发生上消化道出血，且往往对传统治疗方法耐药。本文报告一例弹性假黄瘤患者发生胃出血的病例。对弹性假黄瘤的特征进行了综述，并讨论了这些患者上消化道出血的处理方法。
